Glycosaminoglycan Storage Disorders: A Review
نویسندگان
چکیده
منابع مشابه
Glycosaminoglycan Storage Disorders: A Review
Impaired degradation of glycosaminoglycans (GAGs) with consequent intralysosomal accumulation of undegraded products causes a group of lysosomal storage disorders known as mucopolysaccharidoses (MPSs). Characteristically, MPSs are recognized by increased excretion in urine of partially degraded GAGs which ultimately result in progressive cell, tissue, and organ dysfunction. There are eleven dif...
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ژورنال
عنوان ژورنال: Biochemistry Research International
سال: 2012
ISSN: 2090-2247,2090-2255
DOI: 10.1155/2012/471325